What question did this study set out to answer?

To present the challenges and management strategies for advanced heart failure in a pediatric case of Naxos syndrome.

April 13, 2026The International Journal of Artificial Organs

Decompensated heart failure in an adolescent with Naxos syndrome managed with central ECMO and HeartMate III LVAD: A case report

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Population

14-year-old girl with Naxos syndrome, refractory cardiac decompensation, and malignant ventricular arrhythmia

Design

Case_report

Authors

MAMustafa Akdi AYAyşenur Yılmaz SKSinan Sabit Kocabeyoğlu

Discussion

Member takes

Implication

Central VA-ECMO can serve as an effective bridge to durable LVAD support in pediatric patients with complex inherited arrhythmogenic cardiomyopathies like Naxos syndrome.

Key Points

To present the challenges and management strategies for advanced heart failure in a pediatric case of Naxos syndrome.
Described the case of a 14-year-old girl with Naxos syndrome.
Utilized central veno-arterial ECMO for cardiac decompensation.
Implanted a HeartMate III LVAD as a bridge to further treatment.
Highlighted the multidisciplinary approach in management.
The patient had refractory cardiac decompensation and malignant arrhythmia.
Successful implantation of the HeartMate III LVAD following ECMO support.
Emphasized the effectiveness of ECMO as a bridge to durable circulatory support.

Structured PICO

Population

14-year-old girl with Naxos syndrome, refractory cardiac decompensation, and malignant ventricular arrhythmia (n=1)

Intervention

Central veno-arterial extracorporeal membrane oxygenation (VA-ECMO) followed by HeartMate III left ventricular assist device (LVAD)

Central VA-ECMO can serve as an effective bridge to durable LVAD support in pediatric patients with complex inherited arrhythmogenic cardiomyopathies like Naxos syndrome.

Cite This Study

Akdi et al. (2026) studied this question.

synapsesocial.com/papers/69dc89473afacbeac03eb0d0 https://doi.org/10.1177/03913988261435548

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Implication

Central VA-ECMO can serve as an effective bridge to durable LVAD support in pediatric patients with complex inherited arrhythmogenic cardiomyopathies like Naxos syndrome.