Proximal Ureteral Atresia in a Caribbean Neonate With Multicystic Dysplastic Kidney

Proximal ureteral atresia is an exceedingly rare presentation of congenital or neonatal hydronephrosis. We report the case of a full-term, female neonate born with an abdominal mass. On palpation, the mass occupied the right flank, and CT showed features suggestive of multicystic dysplastic kidney (MCDK). The patient had an ultrasound scan (USS)-guided right nephrostomy insertion for decompression, followed by a dimercaptosuccinic acid (DMSA) scan showing a poorly functional right kidney. The patient underwent nephrectomy, which showed a right MCDK along with proximal ureteral atresia. The patient was discharged on the sixth postoperative day and has been followed up in the outpatient clinic.