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September 10, 2025CureusOpen Access

Pulmonary Hypertension in Sickle Cell Disease: A Case Series

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Authors

NPNgowari PokimaNorthwell HealthSGSunydip GillSUNY Downstate Health Sciences UniversityRMReza MoradiGolestan University

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Implication

This case series uncovers risk factors and current management strategies for pulmonary hypertension in sickle cell disease.

Key Points

  • Diagnosing pulmonary hypertension is critical for effective treatment in patients with sickle cell disease.
  • Elevated tricuspid regurgitant velocity over 2.7 m/second indicates higher mortality risks in sickle cell patients.
  • This case series emphasizes assessing varying etiology in pulmonary hypertension to tailor management effectively.
  • Management strategies for pulmonary hypertension in sickle cell disease are evolving, addressing specific risk factors.

Cite This Study

Pokima et al. (2025) studied this question.

synapsesocial.com/papers/68c23e4fb210217d647915c5https://doi.org/10.7759/cureus.89012
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